Systemic sclerosis or scleroderma is a rare autoimmune disease where the body generates too much collagen. This overproduction of collagen causes thickening and hardening of the skin and other organs.
We’ve put together a list of fast facts about systemic sclerosis with help from the Scleroderma Foundation.
- Scleroderma comes from the Greek words for hard “sclero” and skin “dermo.”
- Almost all systemic sclerosis patients will experience hardening of the skin to some extent, many will also have internal organ involvement.
- There are two main types of systemic sclerosis: diffuse cutaneous scleroderma and limited cutaneous scleroderma.
- Diffuse scleroderma patients can experience skin hardening on any part of their body and are more likely to suffer from organ involvement, particularly the kidneys, lungs, and heart.
- Limited scleroderma patients will generally have less skin hardening and are less likely to suffer from organ involvement.
- Ninety percent of scleroderma patients will also suffer from Raynaud’s phenomenon, which causes the blood vessels in the hands and feet to contract in cold conditions causing pain and discoloration.
- Many scleroderma patients will suffer from esophagus problems including heartburn, GERD, and difficulty swallowing.
- Lung involvement in systemic sclerosis patients can lead to chronic lung conditions such as pulmonary fibrosis and pulmonary hypertension.
- Approximately 15 to 20 percent of patients will develop kidney failure, however if treated early, kidney problems can be addressed.
- Around 10 percent of patients will have heart problems including fluid retention around the heart and disturbances to heart rhythm.
- Muscle and joint pain are both linked to the disease and many patients find they have a secondary autoimmune disease such as rheumatoid arthritis or suffer from fibromyalgia.
Scleroderma News is strictly a news and information website about the disease. It does not provide medical advice, diagnosis or treatment. This content is not intended to be a substitute for professional medical advice, diagnosis, or treatment. Always seek the advice of your physician or other qualified health provider with any questions you may have regarding a medical condition. Never disregard professional medical advice or delay in seeking it because of something you have read on this website.
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